Gale and Ira Drukier Institute for Children's Health
Found 247 results
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2016
Al-Hassnan ZN, Shinwari ZMa, Wakil SM, Tulbah S, Mohammed S, Rahbeeni Z, Alghamdi M, Rababh M, Colak D, Kaya N et al..  2016.  A substitution mutation in cardiac ubiquitin ligase, FBXO32, is associated with an autosomal recessive form of dilated cardiomyopathy.. BMC Med Genet. 17:3.
Kim TWhan, Hong S, Lin Y, Murat E, Joo HM, Kim T, Pascual V, Liu Y-J.  2016.  Transcriptional Repression of IFN Regulatory Factor 7 by MYC Is Critical for Type I IFN Production in Human Plasmacytoid Dendritic Cells.. J Immunol. 197(8):3348-3359.
Blankley S, Graham CM, Turner J, Berry MPR, Bloom CI, Xu Z, Pascual V, Banchereau J, Chaussabel D, Breen R et al..  2016.  The Transcriptional Signature of Active Tuberculosis Reflects Symptom Status in Extra-Pulmonary and Pulmonary Tuberculosis.. PLoS One. 11(10):e0162220.
Ghazi NG, Abboud EB, Nowilaty SR, Alkuraya H, Alhommadi A, Cai H, Hou R, Deng W-T, Boye SL, Almaghamsi A et al..  2016.  Treatment of retinitis pigmentosa due to MERTK mutations by ocular subretinal injection of adeno-associated virus gene vector: results of a phase I trial.. Hum Genet. 135(3):327-43.
2015
Ono JG, Worgall TS, Worgall S.  2015.  Airway reactivity and sphingolipids-implications for childhood asthma.. Mol Cell Pediatr. 2(1):13.
Conejero L, Potempa K, Graham CM, Spink N, Blankley S, Salguero FJ, Pankla-Sranujit R, Khaenam P, Banchereau JF, Pascual V et al..  2015.  The Blood Transcriptome of Experimental Melioidosis Reflects Disease Severity and Shows Considerable Similarity with the Human Disease.. J Immunol. 195(7):3248-3261.
Quigley KJ, Reynolds CJ, Goudet A, Raynsford EJ, Sergeant R, Quigley A, Worgall S, Bilton D, Wilson R, Loebinger MR et al..  2015.  Chronic Infection by Mucoid Pseudomonas aeruginosa Associated with Dysregulation in T-Cell Immunity to Outer Membrane Porin F.. Am J Respir Crit Care Med. 191(11):1250-64.
Wellington AC, Spigland NA, Worgall S, Groves AM.  2015.  Decreasing mean airway pressure as a management strategy for tension pneumatocoeles.. Arch Dis Child Fetal Neonatal Ed. 100(2):F101.
Teruel MN, Gu B, Zhao ML.  2015.  A dynamic picture of protein behavior in cells.. Nat Biotechnol. 33(4):356-7.
Theivanthiran B, Kathania M, Zeng M, Anguiano E, Basrur V, Vandergriff T, Pascual V, Wei W-Z, Massoumi R, Venuprasad K.  2015.  The E3 ubiquitin ligase Itch inhibits p38α signaling and skin inflammation through the ubiquitylation of Tab1.. Sci Signal. 8(365):ra22.
Anandasabapathy N, Breton G, Hurley A, Caskey M, Trumpfheller C, Sarma P, Pring J, Pack M, Buckley N, Matei I et al..  2015.  Efficacy and safety of CDX-301, recombinant human Flt3L, at expanding dendritic cells and hematopoietic stem cells in healthy human volunteers.. Bone Marrow Transplant. 50(7):924-30.
Kamada N, Sakamoto K, Seo S-U, Zeng MY, Kim Y-G, Cascalho M, Vallance BA, Puente JL, Nunez G.  2015.  Humoral Immunity in the Gut Selectively Targets Phenotypically Virulent Attaching-and-Effacing Bacteria for Intraluminal Elimination.. Cell Host Microbe. 17(5):617-27.
Papaspyridonos M, Matei I, Huang Y, André Mdo Rosári, Brazier-Mitouart H, Waite JC, Chan AS, Kalter J, Ramos I, Wu Q et al..  2015.  Id1 suppresses anti-tumour immune responses and promotes tumour progression by impairing myeloid cell maturation.. Nat Commun. 6:6840.
Canesin G, Cuevas EP, Santos V, López-Menéndez C, Moreno-Bueno G, Huang Y, Csiszar K, Portillo F, Peinado H, Lyden DC et al..  2015.  Lysyl oxidase-like 2 (LOXL2) and E47 EMT factor: novel partners in E-cadherin repression and early metastasis colonization.. Oncogene. 34(8):951-64.
Ahrends R, Niewiadomski P, Teruel MN, Rohatgi R.  2015.  Measuring Gli2 Phosphorylation by Selected Reaction Monitoring Mass Spectrometry.. Methods Mol Biol. 1322:105-23.
Wang X, Dubuc AM, Ramaswamy V, Mack S, Gendoo DMA, Remke M, Wu X, Garzia L, Luu B, Cavalli F et al..  2015.  Medulloblastoma subgroups remain stable across primary and metastatic compartments.. Acta Neuropathol. 129(3):449-57.
Bagaitkar J, Pech NK, Ivanov S, Austin A, Zeng MYue, Pallat S, Huang G, Randolph GJ, Dinauer MC.  2015.  NADPH oxidase controls neutrophilic response to sterile inflammation in mice by regulating the IL-1α/G-CSF axis.. Blood. 126(25):2724-33.
Palaniyar N, Mall MA, Taube C, Worgall S, Grasemann H.  2015.  New Developments in Cystic Fibrosis Airway Inflammation.. Mediators Inflamm. 2015:769425.
Jacquemin C, Schmitt N, Contin-Bordes C, Liu Y, Narayanan P, Seneschal J, Maurouard T, Dougall D, Davizon ESpence, Dumortier H et al..  2015.  OX40 Ligand Contributes to Human Lupus Pathogenesis by Promoting T Follicular Helper Response.. Immunity. 42(6):1159-70.
Costa-Silva B, Aiello NM, Ocean AJ, Singh S, Zhang H, Thakur BKumar, Becker A, Hoshino A, Mark MTešić, Molina H et al..  2015.  Pancreatic cancer exosomes initiate pre-metastatic niche formation in the liver.. Nat Cell Biol. 17(6):816-26.
Hoshino A, Costa-Silva B, Shen T-L, Rodrigues G, Hashimoto A, Mark MTesic, Molina H, Kohsaka S, Di Giannatale A, Ceder S et al..  2015.  Tumour exosome integrins determine organotropic metastasis.. Nature. 527(7578):329-35.
Ota A, Kovary KM, Wu OH, Ahrends R, Shen W-J, Costa MJ, Feldman BJ, Kraemer FB, Teruel MN.  2015.  Using SRM-MS to quantify nuclear protein abundance differences between adipose tissue depots of insulin-resistant mice.. J Lipid Res. 56(5):1068-78.